Congenital lung abnormalities are not infrequently seen by non-pediatric radiologists and can often be a source of confusion. It is important for the interpreting radiologist to recognize the various types of congenital lung diseases to allow for a timely diagnosis and institution of appropriate treatment. At the end of this presentation, the audience will feel more comfortable in making an accurate diagnosis when they encounter a study demonstrating congenital lung disease.
Educational Goals / Teaching Points
The goal of this presentation is to use a case based approach to review common congenital lung disease. We hope to highlight the distinguishing characteristics of each of these entities and provide the viewer with an algorithmic approach they can use to help them narrow the differential
Key Anatomic/Physiologic Issues and Imaging Findings/Techniques
We will first describe the normal embryological development of the respiratory system. Next we will do a multi-modality pictorial review of the most common congenital lung diseases including: Pulmonary agenesis, pulmonary aplasia, pulmonary hypoplasia, congenital pulmonary airway malformation, bronchial atresia, bronchogenic cyst, congenital lobar emphysema, pulmonary sequestration, Scimitar syndrome, congenital diaphragmatic herniation, and Swyer-James-MacLeod syndrome. We will focus on highlighting the distinguishing characteristics of each of these entities and treatments for each of these entities.
Congenital lung disease may be seen in adults and thus it is essential for radiologists to be familiar with these entities to be able to distinguish them and guide appropriate therapy.